International Clinical and Medical Case Reports Journal (ISSN: 2832-5788) | Volume 4, Issue 8 | Case Report | Open Access DOI
Hanae Ben Abdenbi*
Hanae Ben Abdenbi*, Kaoutar Znati
Department of Pathology, Ibn Sina Hospital Center, Faculty of Medicine and Pharmacy of Rabat, Mohamed V University, 10100, Rabat, Morocco
*Correspondence to: Hanae Ben Abdenbi
Fulltext PDFErdheim-Chester disease (ECD) is a rare condition classified as a non-Langerhans cell histiocytosis.
We present a case of 40-year-old man with dyspnea and chronic cough. Thoracic CT scan showed bilateral pulmonary consolidations.
Histological study of the CT guided biopsy revealed a proliferation of large cells with histiocytic features. On immunohistochemistry, the CD68 marker showed positive staining and confirmed the histiocytic nature of these large cells, which also expressed CD45, CD79, and CD99. In contrast, the staining of the histiocytic cells was negative for CD1a.
Hanae Ben Abdenbi, Kaoutar Znati. Exclusive Pulmonary Involvement in Erdheim-Chester Disease: A Rare Presentation. Int Clinc Med Case Rep Jour. 2025;4(8):1-3.