International Clinical and Medical Case Reports Journal (ISSN: 2832-5788) | Volume 1, Issue 2 | Case Report | Open Access

MRKH Syndrome and A Better Tomorrow

Chetan Gulati*

Obstetrics and Gynaecology, Dr. D. Y Patil Medical College and Hospital, Pune, India

*Correspondence to: Chetan Gulati 

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Abstract

Vaginal agenesis may present as a single defect in development or associated with other anomalies. It is usually associated with Mayer-Rokitansky-Kuster-Hauser (MRKH) and Androgen Insensitivity Syndromes (AIS). The incidence is about 1 in 4,000-5,000 live female births. The principal aim of treating the congenital absence of vagina is to solve problems of sexual life and reconstruction of vagina.

AIM AND OBJECTIVES

AIM: Treating the congenital absence of vagina to solve problems of sexual life and reconstruction of vagina.

OBJECTIVES: To assess the operative time, blood loss, post-operative pain of surgery. To reconstruct vagina anatomically to establish the patency and calibre of vagina.

METHOD: By surgical intervention

DISCUSSION: A case of MRKH unmarried patient aged 28 years who presented with primary amenorrhea at our institution. -Workup for primary amenorrhea was done which was suggestive of MRKH syndrome. -Surgical intervention was planned accordingly -An artificial mould coated with a fresh amnion graft was created using a 10cc syringe, coated with foam sponge and covered with a condom. -Fresh amnion graft was harvested from a patient and triple washed with normal saline and antibiotics.

CONCLUSION: An adequate length vagina was created and normal sexual activity initiated.

Keywords:

Vaginal agenes; MRKH Syndrome; Uterus

Citation:

Monalisa Sarka , Chetan Gulati, Hemant Deshpande, Shubham Joon. MRKH Syndrome and a Better Tomorrow. Int Clinc Med Case Rep Jour. 2022;1(2):1-7.